Robinow Syndrome : an anesthetic challenge and review of literature

Keywords:

Robinow syndrome ; pediatric anesthesia ; mid facial hypoplasia ; facial dysmophism ; ophthalmic surgery


Published online: Nov 25 2022

https://doi.org/10.56126/ 71.3.7

V. Depal (*), N. Patel (*), A. Singh (*), A. Kumar (**)

(*) All India Institute of Medical Sciences New Delhi, New Delhi, India.
(**) Department of Anaesthesia Lady Hardinge Medical College, New Delhi, India.

Abstract

Robinow Syndrome is characterized by the presence of mesomelic limb shortening, midfacial hypoplasia, hemivertebrae and genital hypoplasia. Multi- organ involvement including cardiac, renal, vertebral dysfunctions have been described.We here report successful anaesthetic management of 1year old boy posted for ophthalmic procedure.